Mental Development and Surgical Prognosis of Pai Syndrome: A Case Report and Review of the Literature.

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Mental Development and Surgical Prognosis of Pai Syndrome: A Case Report and Review of the Literature.

Cleft Palate Craniofac J. 2018 Jan 01;:1055665618771419

Authors: Imai Y, Kure S, Nara C, Takagi N, Tachi M

Abstract
Pai syndrome is a rare congenital disorder, and there are few reports about the long-term prognosis of mental development and surgical results. Here, we report a patient with Pai syndrome who was followed up from birth up to the age of 8 years. Additionally, we review 32 articles and discuss the long-term prognosis of Pai syndrome. In our case, an intracranial lipoma grew a little, but neither epilepsy nor intellectual disabilities occurred. However, she showed attention-deficit/hyperactivity disorder. Furthermore, her nasal airway was gradually obstructed by a residual intranasal polyp.

PMID: 29665340 [PubMed – as supplied by publisher]

via https://www.ncbi.nlm.nih.gov/pubmed/29665340?dopt=Abstract